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Type: Artigo de periódico
Title: Dentomaxillofacial manifestations of mucopolysaccharidosis VI: clinical and imaging findings from two cases, with an emphasis on the temporomandibular joint
Author: Cavaleiro, RMD
Pinheiro, MDR
Pinheiro, LR
Tuji, FM
Feio, PDQ
de Souza, ICN
Feio, RHF
de Almeida, SC
Schwartz, IVD
Giugliani, R
Pinheiro, JJV
Santana-Da-Silva, LC
Abstract: Objectives. Using a clinical survey, panoramic, cone-beam computed tomography (CBCT), and magnetic resonance (MR) imaging, this study was conducted to ascertain primary maxillofacial abnormalities in patients with mucopolysaccharidosis VI (MPS VI). Study design. Two patients previously diagnosed with MPS VI underwent clinical and imaging surveys (panoramic radiographs, CBCT, and MR imaging). Results. Jaw involvement was present in all patients. The most prevalent findings were enlarged marrow spaces, osteopenia, dentigerous cyst-like follicles, effacement of the jaw structures, and osteosclerosis. This is the first study to describe temporomandibular joint (TMJ) involvement for MPS VI. Conclusions. CBCT and MR imaging were needed to observe features that were not clear in conventional radiographs. Both patients reported symptoms in the TMJ and demonstrated involvement during their examinations. A multicenter study is necessary to better document maxillofacial involvement in MPS VI.
Country: EUA
Editor: Elsevier Science Inc
Citation: Oral Surgery Oral Medicine Oral Pathology Oral Radiology. Elsevier Science Inc, v. 116, n. 2, n. E141, n. E148, 2013.
Rights: fechado
Identifier DOI: 10.1016/j.oooo.2013.04.021
Date Issue: 2013
Appears in Collections:Unicamp - Artigos e Outros Documentos

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