Please use this identifier to cite or link to this item: http://repositorio.unicamp.br/jspui/handle/REPOSIP/359014
Type: Artigo
Title: Scleromyxedema: clinical diagnosis and autopsy findings
Author: Bulhoes Sala, Ana Carolina
Cunha, Paulo Rowilson
Lopes Pinto, Clovis Antonio
Xavier de Moraes Alves, Celia Antonia
Paiva, Ingrid Barreto
Vieira Araujo, Ana Paula
Abstract: Scleromyxedema is a rare chronic cutaneous mucinosis of unknown etiology. It is characterized by papular eruption and scleroderma with microscopic evidence of mucin deposition, fibroblast proliferation, and fibrosis. Most patients with scleromyxedema have monoclonal gammopathy and systemic manifestations resulting in significant morbidity and mortality. Several types of treatment have been reported with partial or inconsistent responses. Despite showing unpredictable evolution, systemic consequences of scleromyxedema and treatment side effects may result in death. We describe a rare case of a patient with scleromyxedema without paraproteinemia with systemic involvement that evolved to death despite treatment with cyclophosphamide
Subject: Autópsia
Country: Brasil
Editor: Sociedade Brasileira de Dermatologia
Rights: Aberto
Identifier DOI: 10.1590/abd1806-4841.20164527
Address: https://www.scielo.br/scielo.php?script=sci_arttext&pid=S0365-05962016001100048
Date Issue: 2016
Appears in Collections:FCM - Artigos e Outros Documentos

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