Please use this identifier to cite or link to this item: http://repositorio.unicamp.br/jspui/handle/REPOSIP/26801
Type: Artigo de periódico
Title: Nevoid Basal-Cell Syndrome: literature review and case report in a family
Author: Tincani, Alfio José
Martins, Antônio Santos
Andrade, Ricardo Gomes
Mello Jr., Edgar José Franco
Bueno, Marco Antônio Camargo
Abstract: The Nevoid Basal-Cell Carcinoma Syndrome (NBCC), or as it is also referred to, basal-cell nevus syndrome or Gorlin-Goltz syndrome, is characterized by multiple early-appearing basal cell carcinomas, keratocytosis of the mandible, and anomalies of the ocular, skeletal reproductive system. We describe four patients in the same family, all of them possessing a large number of skin tumors associated with other typical clinical and X-Ray anomalies of NBCC. The definitive treatment of NBCC has yet to be established, however, early diagnosis is very important as well as the periodical follow-up examination of ten patients, mainly due to the transformations in the skin lesions that may occur.
INTRODUÇÃO: A Síndrome do Nevo Basocelular (SNBC), também chamada de Síndrome do Carcinoma Nevóide Basocelular ou Síndrome de Gorlin-Goltz, caracteriza-se por múltiplos carcinomas basocelulares de aparecimento precoce, cistos em mandíbula, além de outras anomalias como as ósseas, problemas oculares e no aparelho reprodutivo. CONCLUSÃO: O tratamento definitivo da SNBC ainda não foi bem estabelecido, porém ressalta-se a importância do diagnóstico precoce, além do seguimento periódico dos pacientes, principalmente devido às transformações das lesões da pele que podem ocorrer.
Subject: Basal-cell carcinoma
Skin tumors
Gorlin-Goltz Syndrome
Editor: Associação Paulista de Medicina - APM
Rights: aberto
Identifier DOI: 10.1590/S1516-31801995000300006
Address: http://dx.doi.org/10.1590/S1516-31801995000300006
http://www.scielo.br/scielo.php?script=sci_arttext&pid=S1516-31801995000300006
Date Issue: 1-Jun-1995
Appears in Collections:Artigos e Materiais de Revistas Científicas - Unicamp

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