Please use this identifier to cite or link to this item: http://repositorio.unicamp.br/jspui/handle/REPOSIP/235515
Type: Outros documentos
Title: Family of crouzon syndrome represents the evolution of the frontofacial monobloc advancement technique: from immediate movement to monobloc distraction to monobloc bipartition distraction
Author: Raposo-Amaral, Cassio Eduardo
Denadai, Rafael
Ghizoni, Enrico
Buzzo, Celso Luiz
Raposo-Amaral, Cesar Augusto
Abstract: Crouzon syndrome (CS) is an autosomal dominant disorder characterized by premature fusion of cranial sutures, midface and supraorbital ridge retrusion, exorbitism, and in some clinical scenarios strabismus, parrot-beaked nose, short upper lip and hypertelorbitism. Treatment of CS is overlapped with the beginning of craniofacial surgery and is grounded on morphologic and functional objectives. The authors reported on the outcomes and complications of family members (mother and 2 siblings) with CS, who were operated on by different techniques of frontofacial advancement and have attained skeletal maturity. Operations were performed in different moments throughout the last 3 decades of craniofacial surgery history. A 10-year-old Crouzon progenitor underwent a monobloc osteotomy with acute advancement, using rigid fixation and bone grafting in the osteotomy sites. An 8-year-old Crouzon daughter underwent gradual lengthening of a monobloc segment, using an external, institutionally made distracter device. In addition, a 10-year-old Crouzon son underwent gradual lengthening of a monobloc segment associated to facial bipartition, using an internal distracter device. After 30 years, the mother presented a mild relapse on the orbit level, but her children had satisfactory stable outcomes. The family members with CS have undergone different modifications of the monobloc approach based on different chronological momentum, from acute monobloc advancement, to monobloc distraction, to monobloc facial bipartition distraction.
Crouzon syndrome (CS) is an autosomal dominant disorder characterized by premature fusion of cranial sutures, midface and supraorbital ridge retrusion, exorbitism, and in some clinical scenarios strabismus, parrot-beaked nose, short upper lip and hypertel
Subject: Transplante ósseo
Craniotomia
Osso frontal
Osteogênese por distração
Osteotomia de Le Fort
Country: Estados Unidos
Editor: Lippincott Williams & Wilkins
Citation: The Journal Of Craniofacial Surgery. v. 26, n. 6, p. 1940-1943, 2015-Sep.
Rights: fechado
Identifier DOI: 10.1097/SCS.0000000000001949
Address: https://journals.lww.com/jcraniofacialsurgery/Fulltext/2015/09000/Family_of_Crouzon_Syndrome_Represents_the.32.aspx
Date Issue: 2015
Appears in Collections:FCM - Artigos e Outros Documentos

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