Please use this identifier to cite or link to this item: http://repositorio.unicamp.br/jspui/handle/REPOSIP/201421
Type: Artigo de periódico
Title: Multiple Desmoid Tumors In A Patient With Gardner's Syndrome - Report Of A Case.
Author: Pinheiro, Lílian Vital
Fagundes, João José
Coy, Cláudio Saddy Rodrigues
Cabello, Cesar
Toro, Ivan
Michellino, Marcelo
Fachina, Paulo Henrique
Ward, Marc
Leal, Raquel Franco
Ayrizono, Maria de Lourdes Setsuko
Abstract: Desmoid tumor (DT) is a common manifestation of Gardner's Syndrome (GS), although it is a rare condition in the general population. DT in patients with GS is usually located in the abdominal wall and/or intra-abdominal cavity. We report a case of a 32 years-old female patient with familial adenomatous polyposis (FAP), who was already submitted to total colectomy and developed multiple DT, located in the abdominal wall and in the left breast. The patient underwent several surgical procedures, with a multidisciplinary team of surgeons. Wide surgical resections of the left breast and the abdominal wall tumors were performed in separate steps. Polypropylene mesh reconstruction and muscle flaps were needed to cover the defects of the thoracic and abdominal walls. After partial necrosis of the adipose-cutaneous flap in the abdomen that required a new skin graft, she had a satisfactory outcome with complete healing of the surgical incisions. DT is frequent in GS, however, breast localization is very rare, with few cases reported in the literature. Recurrence of DT is not negligible, even after a wide surgical resection. GS patients must be followed up closely, and clinical examination, associated with imaging studies, should be performed to detect any signs of tumor. DT represents one of the most significant causes of the morbidity and mortality that affects FAP patients following colectomy. In general, the surgical procedures to excise DT are highly complex, requiring a multidisciplinary team.
Subject: Desmoid Tumor
Familial Adenomatous Polyposis
Gardner's Syndrome
Surgical Approach
Rights: aberto
Identifier DOI: 10.1016/j.ijscr.2014.04.018
Address: http://www.ncbi.nlm.nih.gov/pubmed/24858982
Date Issue: 2014
Appears in Collections:Unicamp - Artigos e Outros Documentos

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