Please use this identifier to cite or link to this item: http://repositorio.unicamp.br/jspui/handle/REPOSIP/102200
Type: Artigo de periódico
Title: Caroli's Disease: 6 Case Studies
Author: Alves De Tommaso A.M.
Moreira Santos D.S.
Hessel G.
Abstract: Caroli's disease is characterized by congenital non-obstructive dilatation of the intrahepatic bile ducts of undefined etiology. It is a rare disease usually affecting the whole liver but it may affect a lobe or a segment (11). This study shows the evolution of 6 cases (2 boys and 4 girls) that were diagnosed with Caroli's disease at a referral service. Their ages ranged from 2 to 16 years - median age 10 years. One of the patients presented with cholangitis, while hepatomegaly was observed in 83% of the cases. Four of the patients presented biliary lithiasis and in one of these cholesterol crystals could be observed in the duodenal secretion. The diagnosis was confirmed in 4 cases by endoscopic retrograde cholangiopancreatography, in 1 by cholangioresonance and 1 by echography. Two of the patients also presented congenital hepatic fibrosis. The outpatient clinic follow-up indicated that all the patients evolved well with the exception of one patient who was selected as a candidate for liver transplantation.
Editor: 
Rights: aberto
Identifier DOI: 
Address: http://www.scopus.com/inward/record.url?eid=2-s2.0-25144482825&partnerID=40&md5=557f513e2392d6dc1059621c24a22ffe
Date Issue: 2003
Appears in Collections:Unicamp - Artigos e Outros Documentos

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